Table 1 Characteristics of life-threatening AOSD
n (%) | |
|---|---|
Characteristics of patients | |
Age, years (median) | 36 (18–64) |
Male | 12 (60%) |
First episode | 18 (90%) |
AOSD features | |
Fever | 20 (100%) |
Rash | 13 (65%) |
Sore throat | 13 (65%) |
Arthromyalgia | 17 (85%) |
Arthritis | 3 (15%) |
Hepatosplenomegaly | 13 (65%) |
Organ manifestations | |
Respiratory | |
Acute respiratory failure | 15 (75%) |
Lung infiltrate | 12 (60%) |
Pleural effusion | 12 (60%) |
Cardiocirculatory | |
Shock | 10 (50%) |
Myocarditis | 8 (40) |
Pericarditis | 10 (50%) |
Tamponade | 3 (16%) |
Hematologic | |
Disseminated intravascular coagulation | 10 (50%) |
Hemophagocytosis | 8 (40%) |
Thrombotic microangiopathy | 1 (5%) |
Other | |
Acute kidney injury | 7 (35%) |
Neurologic dysfunction | 5 (25%) |
Severe hepatitis | 3 (15%) |
Multiple organ failure | 8 (40%) |
Death | 2 (10%) |