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Table 2 Approximate frequencies (%) of major organ involvement

From: Clinical review: Vasculitis on the intensive care unit – part 1: diagnosis

Organ system

WG

MPA

CSS

PAN

Skin

50

40

60

50

Renal

80

90

60–80

30

Pulmonary

90

50

40a

Rare

Ear, nose and throat

90

35

50

Uncommon

Musculoskeletal

60

60

50

50–60

Neurological

30

30

70

60–70b

GI tract

50

50

50

30

Cardiac

10

 

20–40

20–30

  1. aEvidence of pulmonary vasculitis; excludes asthma. bPredominantly mononeuritis multiplex. CSS, Churg–Strauss syndrome; MPA, microscopic polyangiitis; PAN, polyarteritis nodosa; WG, Wegener's granulomatosis. Data compiled from [3,18,20,26,28].